Partial Duplication of Maxilla Associated With Tessier 3 and Incomplete Tessier 6 Cleft: A New Entity

Oblique facial clefts are extremely rare congenital deformities. Partial duplication of maxilla is a rare isolated anomaly. The concurrent existence of maxillary duplication and Tessier clefts has been described previously, specially the Tessier 7 clefts. In presented case, partial duplication of maxilla has occurred associated with Tessier 3 and incomplete Tessier 6 cleft along with cleft palate which might be the first case of its kind till now. Traditionally the correction of oblique facial cleft involved multiple local cheek and nasal flaps in Tessier 3. In presented case the use of a nasal flap was impossible due to significant defect of the lateral nose. An irregular Z plasty of cleft closure was therefore used in first stage. This was followed by extraction of supernumerary teeth present in the duplicated (accessory) maxilla. Resection of the duplicated maxilla and cleft palate closure was performed in second stage.